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O que é GPA na medicina?
A granulomatose com poliangiite é caracterizada por inflamação granulomatosa necrosante, vasculite de pequenos e médios vasos e glomerulonefrite necrosante focal, geralmente crescêntica. Tipicamente, o trato respiratório superior e inferior e os rins são afetados, mas qualquer órgão também pode ser.
O que é poliarterite nodosa?
A poliarterite nodosa (PAN) é uma vasculite necrosante sistêmica caracterizada pela presença de um processo inflamatório agudo e necrose fibrinoide das artérias de pequeno e médio calibre. É uma doença considerada rara, com uma prevalência na população geral de cerca de seis por 100.000 pessoas.
What are some causes of Wegener’s granulomatosis?
Wegener’s granulomatosis (granulomatosis with polyangiitis) is serious but treatable.
What should know about Wegener’s granulomatosis?
Definition and Facts About Granulomatosis with Polyangiitis (Wegener’s) Granulomatosis with polyangiitis is a rare disease in which blood vessels become inflamed (a condition called vasculitis) and localized, nodular collections of abnormal inflammatory cells, known as granulomas, are found in affected tissues.
What is the life expectancy of Wegener’s disease?
The prognosis of wegener’s disease is not good. According to some studies, the life expectancy for it is 67.1+/- 4.4 months. Wegner’s granulomatosis is a kind of vasculitis that commonly involve the kidneys and lungs. The prognosis is dismal when both are involved.
What are some common Wegener’s granulomatosis symptoms?
Other signs and symptoms may include: persistent runny nose. cough , which may include blood. ear infections. joint aches. loss of appetite. malaise, or a general feeling of being unwell. nosebleeds.